A 24 year old girl presented with recurrent nasal obstruction and epistaxis.

1. What is the diagnosis?

2. This cancer originates from?

3. What is the classic finding (s) for the tumor?

4. The typical age for this tumor is?

2. Correct answer:

1. What is the diagnosis?

 Esthesioneuroblastoma

2. This cancer originates from?

The olfactory cells

3. What is the classic finding (s) for the tumor?

Peritumoral cysts, and “Dumbbell” appearance

4. The typical age for this tumor is?

 Bimodal: 20s and 50s


Esthesioneuroblastoma

Essentially a neuroblastoma of the olfactory cells.

KEY FEATURES

- Has a bimodal distributionoccurs 20s and 50s

- Starts growing at the cribriform plate then (usually) grows down and up, waisting in the middle. This creates a dumbbell appearance.

- The characteristic finding is peritumoral cysts at the top. If they want a single diagnosis they have to show you this (otherwise it’s a squamous cell - which is more common).

- They enhance avidly (duh, they are tumors).

- They take up MIBG, because they are basically aneuroblastoma.

Facebook Conversations



Disqus Conversations